Size: 200μL

Storage: Store at -20℃ Valid for 12 months. Avoid freeze / thaw cycles.

Shipping: The product is shipped with ice pack,upon receipt,store it immediately at the temperature recommended.

Exp date: 12 months

Category ID_II: Primary Antibodies

Category ID_III: Polyclonal Antibodies

Abbreviation: HMBS

Target Synonym: HEM3;HMBS;Hydroxymethylbilane synthase;PBG D;PBG-D;PBGD;PORC;Porphobilinogen deaminase;porphyria;acute;Chester type;Pre uroporphyrinogen synthase;Pre-uroporphyrinogen synthase;UPS;Uroporphyrinogen I synthase;Uroporphyrinogen I synthetase

Research Areas: Cancer;Cell Biology;Metabolism;Signal Transduction

Conjugation: Unconjugated

Host: Rabbit

Species reactivity: Human;Mouse;Rat

Application: WB

Isotype: IgG

Clonality: Polyclonal

Clone NO.:

UNIProt ID: P08397

Accession:

Background: This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.

Concentration: 1.08 mg/mL

Immunogen: Fusion protein of human HMBS

Buffer: PBS with 0.05% NaN3 and 40% Glycerol,pH7.4

Purification method: Antigen affinity purification

Dilution: WB 1:500-1:2000

Calculated MW: 39 kDa

ObservedMW: Refer to figures